Long-term follow-up of total abdominal wall reconstruction for prune belly syndrome

Malcolm A Lesavoy1, Eric I Chang, Ahmed Suliman

  • 1Los Angeles, Calif. From the Division of Plastic and Reconstructive Surgery, University of California, Los Angeles Medical Center.

Insights

This study shows that the double-breasted technique for total abdominal wall reconstruction is a safe and effective method for treating prune belly syndrome (PBS). The procedure offers excellent cosmetic results and patient satisfaction with long-term durability.

Area of Science:

  • Plastic Surgery
  • Pediatric Surgery
  • Congenital Malformations

Background:

  • Prune belly syndrome (PBS) is a rare congenital disorder characterized by abdominal wall muscle deficiency, cryptorchidism, and genitourinary anomalies.
  • Reconstructing the abdominal wall in PBS patients presents significant surgical challenges.

Purpose of the Study:

  • To evaluate the long-term safety, durability, and cosmetic outcomes of a specific total abdominal wall reconstruction technique in patients with prune belly syndrome.
  • To present one of the largest patient series with the longest follow-up for this reconstructive approach.

Main Methods:

  • The study reviewed the experience of 20 patients undergoing total abdominal wall reconstruction using a previously described "double-breasted" medial fascial advancement technique.
  • This method allowed for simultaneous urinary tract reconstruction and bilateral orchiopexy, with preservation of the umbilicus.

Main Results:

  • A mean follow-up of 20.4 years revealed no major complications in the 20 patients.
  • All patients reported high satisfaction with their postoperative cosmetic and functional results.

Conclusions:

  • Total abdominal wall reconstruction utilizing the double-breasted technique is a safe and durable surgical option for prune belly syndrome.
  • This approach yields excellent cosmetic outcomes and high patient satisfaction in the long term.
Abstract