Extraperitoneal presentation of pseudomyxoma peritonei as retroperitoneal invasion with skin fistula-a case report

Lu Chang-Yun1, Hsieh Mao-Chi, Yutaka Yonemura

  • 1Dept. of General Surgery, Wang Fang Hospital, Taipei Medical University, Taiwan.

Insights

Pseudomyxoma peritonei (PMP) is a rare condition. This case highlights PMP presenting in the retroperitoneum with a spontaneous skin fistula, a very uncommon occurrence.

Area of Science:

  • Oncology
  • Gastroenterology
  • Surgical Pathology

Background:

  • Pseudomyxoma peritonei (PMP) typically presents with mucinous ascites and peritoneal implants.
  • Retroperitoneal involvement is an exceptionally rare manifestation of PMP.

Observation:

  • A unique case of PMP with a primary retroperitoneal presentation is described.
  • The patient spontaneously developed a cutaneous fistula, a complication rarely associated with PMP.

Findings:

  • This report details the eighth documented instance of PMP involving the retroperitoneum.
  • The spontaneous development of a skin fistula in this context is a significant clinical observation.

Implications:

  • This case expands the understanding of PMP's anatomical variations.
  • It underscores the importance of considering rare presentations in the differential diagnosis of retroperitoneal masses and fistulas.
  • Further investigation into the mechanisms of fistula formation in PMP may be warranted.

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