Chronic thromboembolic pulmonary hypertension (CTEPH): updated Recommendations of the Cologne Consensus Conference

Heinrike Wilkens1, Irene Lang, Jürgen Behr

  • 1Clinic for Internal Medicine V, Saarland University Hospital, Homburg. heinrike.wilkens@uks.eu

Insights

Chronic thromboembolic pulmonary hypertension (CTEPH) is a treatable form of pulmonary hypertension (PH). Early diagnosis via ventilation/perfusion scans and referral to specialized centers improve patient outcomes.

Area of Science:

  • Cardiology
  • Pulmonology
  • Vascular Surgery

Background:

  • Pulmonary hypertension (PH) encompasses various conditions, including chronic thromboembolic pulmonary hypertension (CTEPH).
  • CTEPH is a potentially curable subset of PH, treatable with pulmonary endarterectomy (PEA).
  • Current management often involves underdiagnosis and suboptimal treatment of CTEPH.

Framework:

  • The 2009 European Guidelines provide a framework for CTEPH diagnosis and treatment.
  • Implementation of these guidelines is critical for effective patient management.
  • This recommendation updates and comments on the European guidelines, incorporating recent advancements.

Implementation:

  • Ventilation/perfusion (V/Q) lung scans are the recommended screening tool for unexplained PH.
  • CT angiography can also identify signs suggestive of CTEPH.
  • Patients with suspected CTEPH require referral to specialized centers for expert evaluation and management.

Implications:

  • Timely diagnosis and appropriate management of CTEPH can lead to a cure.
  • Surgical assessment by an experienced PEA surgeon is essential for determining operability.
  • Improved adherence to guidelines and updated information can enhance clinical practice and patient outcomes.

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