Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Related Experiment Videos

Linear scleroderma associated with ptosis and motility disorders.

M S Suttorp-Schulten1, L Koornneef

  • 1Department of Ophthalmology, Academic Medical Centre, Amsterdam, The Netherlands.

The British Journal of Ophthalmology
|November 1, 1990
PubMed
Summary

Linear scleroderma en coup de sabre is a rare condition causing progressive ptosis and eye muscle disorders in children. This case highlights the importance of recognizing its ocular manifestations.

Related Concept Videos

You might also read

Related Articles

Articles linked to this work by shared authors, journal, and citation graph.

Sort by
Same author

Recent developments in the treatment of posterior uveitis.

Ocular immunology and inflammation·2012
Same author

Corneal astigmatism in Graves' ophthalmopathy.

Eye (London, England)·2005
Same author

Diabetes mellitus: a risk factor affecting visual outcome in branch retinal vein occlusion.

European journal of ophthalmology·2003
Same author

The intranasal ostium after external dacryocystorhinostomy and the internal opening of the lacrimal canaliculi.

Orbit (Amsterdam, Netherlands)·2002
Same author

Bony orbital development after early enucleation in humans.

The British journal of ophthalmology·2001
Same author

Delayed diagnosis of homocystinuria as a cause of vascular retinal occlusion in young adults.

The British journal of ophthalmology·1999

Area of Science:

  • Ophthalmology
  • Dermatology
  • Pediatrics

Background:

  • Linear scleroderma en coup de sabre is a rare autoimmune condition characterized by localized scleroderma.
  • Ocular involvement is an uncommon but significant manifestation, particularly in pediatric cases.

Observation:

  • An 11-year-old girl presented with progressive ptosis and a motility disorder affecting her right eye.
  • The clinical presentation led to the diagnosis of linear scleroderma en coup de sabre.

Findings:

  • Computed tomography (CT) scans revealed atrophy of the levator palpebrae superioris and superior rectus muscles in the affected eye.
  • This muscular atrophy correlated with the observed ophthalmoplegia and ptosis.

Implications:

Related Experiment Videos

  • This case underscores the need for ophthalmological evaluation in children diagnosed with linear scleroderma en coup de sabre.
  • Early recognition of ocular complications can guide timely management and potentially prevent further visual impairment.