Heterotopic pancreas causing duodenal obstruction in a patient previously treated for choledochal cyst

Vidyanand P Deshpande1, B V Raghunath, Yogesh K Sarin

  • 1Department of Paediatric Surgery, Maulana Azad Medical College and Associated Lok Nayak Hospital, New Delhi, India.

Insights

A rare case of a 9-year-old boy with duodenal pancreatic rest causing obstruction, previously treated for a choledochal cyst, highlights the unusual co-occurrence of these pediatric conditions. This surgical case underscores the rarity of encountering both heterotopic pancreas and choledochal cysts in the same child.

Area of Science:

  • Pediatric Surgery
  • Gastroenterology
  • Developmental Biology

Background:

  • Choledochal cysts are congenital dilations of the bile ducts, commonly presenting in childhood.
  • Heterotopic pancreas, or ectopic pancreatic tissue, can occur throughout the gastrointestinal tract, including the duodenum.
  • While both conditions are known in pediatric populations, their simultaneous presentation is exceptionally uncommon.

Observation:

  • A 9-year-old male patient experienced duodenal obstruction due to a pancreatic rest (heterotopic pancreas).
  • The patient had a history of choledochal cyst treated surgically at 4 months of age.
  • This presentation marks a metachronous occurrence of both conditions in the same individual.

Findings:

  • The duodenal pancreatic rest caused significant obstruction requiring surgical management.
  • The case confirms the possibility, though extreme rarity, of a child having both a history of choledochal cyst and a heterotopic pancreas presenting later in life.
  • Surgical intervention was successful in relieving the obstruction.

Implications:

  • This case expands the understanding of rare congenital anomalies in children.
  • It emphasizes the importance of considering diverse gastrointestinal pathologies in pediatric patients with complex medical histories.
  • Further research into the embryological origins and potential links between these two conditions may be warranted.

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