Type B interrupted left aortic arch with isolated right subclavian artery

Area of Science:

• Cardiology
• Congenital Heart Disease
• Pediatric Cardiology

Background:

• Interrupted aortic arch is a rare congenital heart malformation with an incidence of approximately 3 per 1 million births.
• Type B interrupted aortic arch, characterized by interruption between the left carotid and left subclavian arteries, is the most common subtype.
• Congenital heart defects require ongoing research into their varied presentations and underlying mechanisms.

Observation:

• This report presents an exceptionally rare anatomical variation of interrupted aortic arch.
• The observed case involved a left-sided Type B interrupted aortic arch.
• A unique feature was the isolation of the right subclavian artery, which originated from the right pulmonary artery.

Findings:

• The case highlights an extremely rare variant of interrupted aortic arch.
• The specific anatomical anomaly involved a left-sided Type B interruption combined with right subclavian artery isolation.
• The right subclavian artery's origin from the right pulmonary artery is a critical finding.

Implications:

• This case expands the known spectrum of interrupted aortic arch malformations.
• Understanding such rare variations is crucial for accurate diagnosis and surgical planning in pediatric cardiology.
• Further investigation into the embryological basis of these rare anomalies may provide new insights.