Symptomatic giant left atrial aneurysm in a child: a rare entity

N Awasthy1, M Tomar, S Radhakrishnan

  • 1Department of Pediatric Cardiology, Escorts Heart Institute and Reseach Center (EHIRC), Okhla road, New Delhi, 110025, India.

Insights

Isolated left atrial aneurysms are rare, especially in children. This case highlights a fatal outcome in a 2-year-old boy with a large left atrial appendage aneurysm, emphasizing the need for further research into pediatric cases.

Area of Science:

  • Cardiology
  • Pediatric Surgery
  • Medical Case Reports

Background:

  • Isolated left atrial aneurysms are uncommon cardiovascular conditions.
  • Diagnosis typically occurs in adults aged 20-40 years.
  • Pediatric cases of left atrial aneurysms are exceptionally rare in medical literature.

Purpose of the Study:

  • To report a rare case of isolated left atrial appendage aneurysm in a pediatric patient.
  • To discuss the clinical presentation, management, and outcome of this rare condition in a child.
  • To review and compare the case with existing English literature on pediatric left atrial aneurysms.

Main Methods:

  • Case presentation of a 2-year-old boy with respiratory distress and edema.
  • Echocardiographic evaluation revealing a large left atrial appendage aneurysm and severe left ventricle dysfunction.
  • Surgical resection of the aneurysm.
  • Intraoperative findings and postoperative course monitoring.

Main Results:

  • The patient presented with irritability, respiratory distress, and pedal edema.
  • Echocardiography confirmed a large left atrial appendage aneurysm with significant left ventricle dysfunction.
  • Postoperative complications included low cardiac output state and frequent arrhythmias.
  • The patient expired on postoperative day 7.

Conclusions:

  • This case underscores the rarity and potential severity of left atrial appendage aneurysms in the pediatric population.
  • Despite surgical intervention, the patient experienced a fatal outcome, highlighting the challenges in managing such rare conditions.
  • Further research and case reporting are crucial for understanding and improving outcomes for pediatric left atrial aneurysms.

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