[Cystic lymphatic malformation of the pancreas in a 13-month-old child]

María G Salvo1, Brian M Cavagnari, José H Méndez

  • 1Departamento de Pediatría, Hospital Alemán, Ciudad Autónoma de Buenos Aires.

Insights

Pancreatic lymphatic malformations are rare in children. This case highlights potential complications after surgical resection, suggesting a need to explore non-surgical management for these pancreatic cysts.

Area of Science:

  • Pediatric Surgery
  • Vascular Anomalies
  • Gastrointestinal Surgery

Background:

  • Lymphatic malformations (LMs) arise from abnormal lymphatic development, causing lymph flow obstruction and cyst formation.
  • While commonly found in the neck/axilla (95%), pancreatic LMs are exceptionally rare in pediatric patients.
  • Distinguishing pancreatic LMs from other cystic pancreatic masses is crucial for appropriate management.

Observation:

  • A 13-month-old child presented with a rare pancreatic head lymphatic malformation.
  • Surgical resection via pancreaticoduodenectomy was performed.
  • The patient experienced persistent chylous drainage post-surgery, leading to immunodeficiency and sepsis.

Findings:

  • Pancreaticoduodenectomy for pancreatic head LMs can lead to severe complications like chylous drainage and sepsis.
  • The case underscores the challenges in managing pediatric pancreatic cystic lesions.
  • Non-surgical approaches warrant consideration for pancreatic lymphatic malformations.

Implications:

  • This case suggests that surgical intervention for pancreatic head LMs may carry significant risks in children.
  • Further research into conservative or minimally invasive treatments is needed.
  • Improved diagnostic and therapeutic strategies are required for rare pediatric pancreatic cystic masses.