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[Lipid storage myopathy. Report of 2 cases]
1Department of Neurology, Beijing Friendship Hospital.
Abstract:
This paper reports two cases of lipid storage myopathy. Light microscopic studies of muscle biopsy materials showed excessive amounts of neutral fatty droplets under oil red O staining. Electron-microscopic studies showed that the fatty droplets were situated in the myofibrils, under the sarcolemma or even in lines. Symptoms of the patients were improved after treatment with prednisone. The clinical, pathological and electromyographic characteristics of both types (I and II) of lipid storage myopathy are reviewed.
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