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[Kyrle disease--a case report]
B Sorhage1, H J Glowania, R Schäfer
1Abteilung für Dermatologie und Venerologie, Bundeswehrzentralkrankenhaus Koblenz.
Summary
This study details Kyrle's disease, a rare genodermatosis characterized by unique hyperkeratotic plugs. Effective treatment involves vitamin A acid therapy, addressing this inherited skin condition.
Area of Science:
- Dermatology
- Genetics
- Histopathology
Background:
- Kyrle's disease (hyperkeratosis follicularis et parafollicularis in cutem penetrans) is a rare genodermatosis.
- It presents with distinctive clinical and histological features.