Combined bladder exstrophy and epispadias repair

Ranjit Chaudhary1, Ashwin Apte, Rajkumar Mehta

  • 1Department of Surgery, Unit of Urology, People's College of Medical Sciences, Bhopal, India.

BMJ Case Reports
|June 9, 2012
PubMed

Insights

This study details a successful combined bladder exstrophy and epispadias repair in a 2-year-old boy. The surgical approach achieved good cosmetic results and functional urinary continence, with a minor fistula successfully managed.

Area of Science:

  • Pediatric Urology
  • Reconstructive Surgery
  • Congenital Anomalies

Background:

  • Exstrophy-epispadias complex is a rare congenital condition requiring complex surgical correction.
  • Early intervention is crucial for optimal functional and cosmetic outcomes in affected children.
  • This case involves a 2-year-old male with untreated bladder exstrophy and epispadias.

Observation:

  • The patient underwent a combined bladder exstrophy and epispadias repair under general anesthesia.
  • Surgical procedures included bilateral anterior innominate and vertical iliac osteotomy due to wide pubic diastasis.
  • A modified Cantwell-Ransley repair was utilized for urethroplasty and penile reconstruction.

Findings:

  • The repair resulted in excellent cosmetic outcomes and good approximation of pubic and rectus muscles.
  • Post-operatively, the patient achieved urethal voiding, with a small penopubic fistula noted and subsequently managed.
  • Urine culture remained sterile, and the patient was discharged on prophylactic antibiotics.

Implications:

  • This case highlights the efficacy of a combined surgical approach for complex bladder exstrophy and epispadias.
  • Successful reconstruction can lead to improved cosmetic appearance and urinary function in affected children.
  • Further follow-up is essential to monitor long-term outcomes and address any potential complications.

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