Related Experiment Video
Updated: May 20, 2026

Intracoronary Acetylcholine Provocation Testing for Assessment of Coronary Vasomotor Disorders
Published on: August 18, 2016
Is it acute coronary syndrome or Churg-Strauss syndrome?
Patompong Ungprasert1, Narat Srivali, Wisit Cheungpasitporn
1Department of Internal Medicine, Bassett Medical Center, Cooperstown, NY 13326, USA.
Insights
Churg-Strauss syndrome (CSS), a rare vasculitis, can cause life-threatening heart issues. This case highlights eosinophilic myopericarditis as a critical cardiac manifestation of CSS.
Area of Science:
- Cardiology
- Rheumatology
- Pathology
Background:
- Churg-Strauss syndrome (CSS) is a rare systemic vasculitis.
- CSS typically presents with asthma, chronic rhinosinusitis, and eosinophilia.
- Cardiac involvement in CSS, though not always initial, is a significant cause of mortality.
Observation:
- A 72-year-old male presented with chest pain.
- Diagnostic workup led to a diagnosis of CSS.
- Biopsy confirmed eosinophilic myopericarditis.
Findings:
- The patient was diagnosed with CSS.
- Biopsy confirmed eosinophilic myopericarditis, a severe cardiac manifestation.
- Literature review on cardiac involvement in CSS was conducted.
Implications:
- Early recognition of cardiac involvement in CSS is crucial for patient outcomes.
- Eosinophilic myopericarditis represents a major cause of morbidity and mortality in CSS.
- This case underscores the importance of considering cardiac evaluation in CSS patients presenting with chest pain.
Abstract:
Churg-Strauss syndrome (CSS) is a rare vasculitic disorder characterized by chronic rhinosinusitis, asthma, and persistent eosinophilia. Although not a usual prominent initial presentation, cardiac involvement is a major cause of morbidity and mortality in patients with CSS. We report a case of a 72-year-old white man who presented with chest pain and was subsequently diagnosed with CSS with biopsy-proven eosinophilic myopericarditis. We have also included a review of the literatures on cardiac involvement in CSS.
More Related Videos
Related Concept Videos
Acute Coronary Syndrome I: Introduction
Acute Coronary Syndrome II: Pathophysiology and Clinical Manifestations
Acute Coronary Syndrome III: Diagnostic Studies
Acute Coronary Syndrome V: Nursing Management
Acute Coronary Syndrome IV: Interprofessional Care
Coronary Artery Disease III: Clinical Manifestations

