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Novel and Innovative Hybrid Technique for Type A Aortic Dissection
Published on: March 28, 2025
Congenital pericardial defect with ruptured acute type A aortic dissection
Masato Furui1, Takeki Ohashi, Yasutaka Hirai
1Department of Cardiovascular Surgery, Nagoya Tokushukai General Hospital, Kasugai, Aichi, Japan.
Insights
Congenital pericardial defects can complicate acute type A aortic dissection, leading to massive hemothorax instead of cardiac tamponade. Considering these defects is crucial for accurate diagnosis and surgical planning in such cases.
Area of Science:
- Cardiovascular Surgery
- Thoracic Surgery
- Medical Diagnostics
Background:
- Acute type A aortic dissection is a life-threatening condition requiring prompt surgical intervention.
- Congenital pericardial defects are rare anomalies that can alter the clinical presentation of cardiovascular emergencies.
Observation:
- Two cases of acute type A aortic dissection with congenital pericardial defects are presented.
- Patients presented with massive hemothorax, not cardiac tamponade, due to the pericardial defect.
- A review of six similar cases revealed a consistent pattern of hemothorax without tamponade.
Findings:
- Congenital pericardial defects allow direct rupture into the pleural space, causing hemothorax.
- The presence of hemothorax can mimic other conditions and complicate surgical decision-making.
- Patients with these defects may not exhibit classic signs of cardiac tamponade.
Implications:
- Preoperative identification of congenital pericardial defects is essential in patients with acute type A aortic dissection and hemothorax.
- This awareness can prevent diagnostic confusion and guide appropriate surgical strategies.
- Understanding this association improves management of complex aortic dissections.
Abstract:
We report 2 cases of congenital pericardial defect with ruptured acute type A aortic dissection. Case 1: An 83-year old man presented with sudden chest and back pain, and computed tomography (CT) showed acute aortic dissection with left pleural massive effusion. Because of his unstable haemodynamic condition with low blood pressure, an emergency operation was performed. We observed small amounts of bloody pericardial effusion, massive left-sided bloody pleural effusion and a partial left-sided pericardial defect of the pulmonary artery. The ascending aorta was replaced. The postoperative course was uneventful. Case 2: A 79-year old man presented with fainting followed by cardiac arrest and was resuscitated. Chest CT showed acute aortic dissection and massive haemothorax. Emergency operation was attempted, but was given up. We observed partial left-sided pericardial defect of the pulmonary artery. Further, we reviewed 6 cases of congenital pericardial defect with ruptured acute aortic dissection, including our 2 cases. In all the cases, the patients did not develop cardiac tamponade but had massive haemothorax due to congenital pericardial defects leading to confusion in diagnoses and surgical strategies. Therefore, it may be necessary to consider congenital pericardial defects before performing an operation in case of acute type A aortic dissection with massive haemothorax.
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