Chordoma metastatic to the ovary

We report a case of sacral chordoma that metastasized to the ovary 31/2 years after initial excision. The ovarian metastasis was the initial evidence of recurrent disease and had to be differentiated from several primary ovarian neoplasms whose appearance was simulated to some extent, particularly a juvenile granulosa cell tumor and an epithelioid smooth-muscle tumor. This case illustrates a heretofore unreported (to our knowledge) metastatic site of chordoma, whose patterns of spread are briefly reviewed.