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Unusual case of new-onset heart failure due to cor triatriatum sinister
Ana Belén Méndez1, Teresa Colchero, Joan Garcia-Picart
1Hospital de Sant Pau, Cardiology, Mas Casanovas, 90, Barcelona 08041, Spain. amendezfe@santpau.cat
Insights
A rare congenital heart defect, cor triatriatum sinister, can cause heart failure in adults. This case highlights successful percutaneous balloon dilatation as an alternative treatment.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Cardiac Surgery
Background:
- Cor triatriatum sinister is a rare congenital heart anomaly, affecting 0.1% of congenital heart disease cases.
- It is seldom diagnosed in adult patients and can mimic severe mitral stenosis.
- The condition involves a fibromuscular membrane dividing the left atrium into two chambers.
Observation:
- A 30-year-old man presented with acute left heart failure.
- Diagnosis revealed cor triatriatum sinister, a rare congenital defect.
- The anomaly presented as a membrane obstructing pulmonary venous return.
Findings:
- The fibromuscular membrane created two left atrial chambers with limited communication.
- Obstructive membrane led to elevated venous and arterial pressures, causing heart failure.
- Percutaneous balloon dilatation was performed as a treatment intervention.
Implications:
- This case demonstrates the successful use of balloon dilatation for cor triatriatum sinister.
- Percutaneous therapy offers a viable alternative to surgical excision for this rare anomaly.
- Early diagnosis and intervention can improve outcomes for adult patients with cor triatriatum sinister.
Abstract:
We report the case of a 30-year old man who came to the emergency department of our hospital with acute left heart failure, and was diagnosed with a rare congenital anomaly (cor triatriatrum sinister), which can mimic a severe mitral stenosis. Cor triatriatum sinister is a rare anomaly (0.1% of all cases of congenital heart disease) that is seldom diagnosed in adult patients. The hallmark of this congenital defect is the presence of a fibromuscular membrane that divides the left atrium (LA) into two chambers: a postero-superior chamber into which the pulmonary veins drain and an infero-anterior chamber (true LA) containing the mitral valve and atrial appendage. Both chambers communicate through a membrane in which one or more drain holes can be found. When the hole is significantly obstructive, it results in increased venous and arterial pressures. Even though the definitive treatment of cor triatriatum is the surgical excision of the membrane, we present a balloon dilatation case with a good response to percutaneous therapy, both initially and in the ensuing months.
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