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Midline cervical cleft: A report of two cases
Somnath Saha1, Saibal Misra, Vedula Padmini Saha
1Medical College Hospital, 700 073 Kolkata, India.
Summary
Congenital midline cervical cleft is a rare birth defect. Diagnosis involves specific features like caudal fistula openings and early fluid discharge, with surgical management discussed for two cases.
Area of Science:
- Pediatric Surgery
- Congenital Anomalies
- Developmental Biology
Background:
- Congenital midline cervical cleft is an uncommon congenital anomaly.
- It presents with distinct diagnostic features observable from the neonatal period onwards.
Purpose of the Study:
- To describe the cardinal diagnostic features of congenital midline cervical cleft.
- To report two cases of this anomaly and review their surgical management.
Main Methods:
- Review of clinical presentation and diagnostic criteria for congenital midline cervical cleft.
- Case report of two patients with congenital midline cervical cleft.
- Literature review on the surgical management of this condition.
Main Results:
- Key diagnostic features include caudal fistula openings, intermittent neonatal serous discharge, superior nipple-like appearance, and later scarring with minimal neck contracture.
- Two cases illustrating these features were identified and managed surgically.
Conclusions:
- Congenital midline cervical cleft diagnosis relies on a combination of specific clinical signs.
- Effective surgical management is crucial for addressing this rare congenital anomaly.