Susac's syndrome: a case of simultaneous development of all three components of the triad

Ayhan Ozturk1, Yildiz Degirmenci, Murat Tunc

  • 1Duzce University College of Medicine, Department of Neurology, Duzce, Turkey.

Susac's syndrome is characterized by the clinical triad of encephalopathy, branch retinal artery occlusions and sensorineural hearing loss. We here report a case of 46 year old woman with a sudden diminution in visual acuity at the left eye, headache and decreased hearing at the right ear with mild confusion considered as Susac's syndrome with complete triad. Although it's a relatively rare entity, it should be kept in mind in differential diagnosis of the neurological disorders, especially in women in 20- to 40-year of age presenting with acute hearing loss.

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