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Middle aortic syndrome caused by Takayasu arteritis
1Department of Pediatrics, Lokmanya Tilak Municipal -General Hospital and Medical College, Sion, Mumbai, India.
Heart Views : the Official Journal of the Gulf Heart Association
|November 28, 2012
Summary
Middle aortic syndrome, a rare narrowing of the aorta, can be caused by Takayasu arteritis. This case highlights an 8-year-old girl with this condition.
Area of Science:
- Cardiovascular Medicine
- Pediatric Rheumatology
- Vascular Biology
Background:
- Middle aortic syndrome (MAS) is a rare vascular condition.
- It involves diffuse narrowing of the thoracic and/or abdominal aorta.
- MAS can be congenital or acquired.
Observation:
- An 8-year-old girl presented with symptoms indicative of MAS.
- Diagnostic workup revealed diffuse narrowing of the aorta.
- Takayasu arteritis was identified as the underlying cause.
Findings:
- The patient was diagnosed with middle aortic syndrome.
- The etiology was confirmed as Takayasu arteritis.
- This case illustrates a pediatric presentation of MAS secondary to vasculitis.
Implications:
- Early diagnosis and management of Takayasu arteritis are crucial in pediatric MAS.
- Understanding acquired causes of MAS is important for comprehensive patient care.
- This case contributes to the literature on rare pediatric aortic diseases.
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