Emergency department visits in children with hemophilia

Bülent Özgönenel1, Ayesha Zia, Michael U Callaghan

  • 1Division of Hematology/Oncology, Carman Ann Adams Children's Hospital of Michigan, Wayne State University, Detroit, Michigan 48201, USA. bulentozgonenel@yahoo.com

Pediatric Blood & Cancer
|November 30, 2012
PubMed

Insights

Pediatric emergency departments are vital for hemophilia care, managing bleeding, infections, and initial diagnoses. This study highlights their role in providing essential after-hours treatment and critical care for children with hemophilia.

Area of Science:

  • Pediatric Emergency Medicine
  • Hematology
  • Pediatric Critical Care

Background:

  • Pediatric emergency department (ED) management is crucial for hemophilia care.
  • Bleeding and central venous catheter (CVC)-related infections are significant complications.

Purpose of the Study:

  • To examine overall ED utilization by children with hemophilia.
  • To investigate ED visits related to injury, bleeding, and CVC-related bloodstream infections.

Main Methods:

  • Retrospective review of electronic medical records.
  • Analysis of ED visits over a 5-year period (January 2006-December 2010).

Main Results:

  • 536 ED visits from 84 male patients with hemophilia.
  • Primary reasons for visits: injury/bleeding (61.2%), suspected CVC infection (11.8%).
  • Intracranial hemorrhage occurred in 5 visits; 5.4% of visits were bloodstream infections.

Conclusions:

  • Pediatric EDs are indispensable for hemophilia care.
  • EDs manage life-threatening conditions like intracranial hemorrhage and CVC infections.
  • EDs facilitate diagnosis in previously undiagnosed patients and provide after-hours care.
Abstract

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