Pulmonary artery sling and tracheal bronchus presenting in a 2-year-old child

Marlina Lovett1, Daniel Entrikin, Ross Ungerleider

  • 1Division of Pediatric Cardiothoracic Surgery, Brenner Children's Hospital, Wake Forest Baptist Health, Winston-Salem, North Carolina, USA.

Insights

Pulmonary artery sling, a rare congenital vascular anomaly, can cause airway obstruction. This case details the surgical correction of tracheal stenosis in a two-year-old with this condition.

Area of Science:

  • Cardiovascular Surgery
  • Pediatric Pulmonology
  • Congenital Vascular Malformations

Background:

  • Pulmonary artery sling is a rare congenital anomaly where the left pulmonary artery arises abnormally from the right pulmonary artery.
  • This anatomical variation can lead to extrinsic compression of the airway, particularly the trachea.
  • Symptoms typically manifest in early infancy, presenting as respiratory distress.

Observation:

  • A two-year-old patient presented with symptoms indicative of tracheal stenosis.
  • The patient was diagnosed with an associated pulmonary artery sling and a tracheal bronchus.
  • This combination presented a complex surgical challenge due to the atypical vascular anatomy and airway compromise.

Findings:

  • Surgical correction of the tracheal stenosis was successfully performed.
  • The underlying pulmonary artery sling and tracheal bronchus were addressed during the procedure.
  • Post-operative recovery was uneventful, with significant improvement in respiratory function.

Implications:

  • This case highlights the importance of considering vascular anomalies in pediatric airway obstruction.
  • Successful surgical intervention can significantly improve outcomes for patients with complex congenital conditions.
  • Further research into the management of pulmonary artery sling with associated airway malformations is warranted.

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