Life-threatening obstructive sleep apnea caused by adenoid hypertrophy in an infant with noonan syndrome

Sonia Khirani1, Nicolas Leboulanger, Adriana Ramirez

  • 1IP Santé, 94200 Ivry sur Seine, France ; Pediatric Pulmonary Department, AP-HP, Hôpital Armand Trousseau, 75012 Paris, France.

Insights

Adenoidectomy can be risky for young children with health issues. This case shows successful adenoidectomy resolved life-threatening sleep apnea in a 15-month-old with Noonan syndrome.

Area of Science:

  • Pediatric Surgery
  • Otolaryngology
  • Genetics

Background:

  • Adenoidectomy is a frequent pediatric surgery with debated efficacy.
  • Children under 3, those with comorbidities, or severe obstructive sleep apnea face higher risks.
  • Hypertrophy of adenoids can cause severe obstructive sleep apnea.

Purpose of the Study:

  • To report a case of successful adenoidectomy in a high-risk pediatric patient.
  • To highlight the resolution of life-threatening obstructive sleep apnea after adenoidectomy.

Main Methods:

  • Case report of a 15-month-old boy with Noonan syndrome.
  • Diagnosis of life-threatening obstructive sleep apnea due to adenoid hypertrophy.
  • Surgical intervention: adenoidectomy.

Main Results:

  • The patient experienced complete resolution of obstructive sleep apnea post-surgery.
  • No significant postoperative respiratory morbidity was observed.

Conclusions:

  • Adenoidectomy can be a life-saving intervention for obstructive sleep apnea in specific pediatric cases.
  • Careful patient selection and risk assessment are crucial for adenoidectomy outcomes.
  • This case underscores the benefits of adenoidectomy in complex pediatric cases with severe obstructive sleep apnea.

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