Left hepatic vein and persistent left superior vena cava drainage into the coronary sinus with subaortic valve...

Area of Science:

• Cardiology
• Vascular Surgery
• Medical Imaging

Background:

• Persistent left superior vena cava (PLSVC) is a rare congenital anomaly.
• PLSVC is often associated with congenital heart disease and conduction abnormalities.
• Left hepatic vein drainage into the coronary sinus is an exceptionally rare venous anomaly.

Observation:

• A 19-year-old female presented with shortness of breath.
• Computed tomography angiogram revealed PLSVC and left hepatic vein drainage into the coronary sinus.
• The patient had a history of subaortic valve stenosis, treated at ages 2 and 8.

Findings:

• This case represents an extremely rare combination of PLSVC and left hepatic vein drainage into the coronary sinus.
• The co-occurrence of these vascular anomalies with subaortic valve stenosis is highly unusual.
• Literature review identified only two prior cases with this specific combination of anomalies.

Implications:

• Recognition of these rare thoracic venous anomalies is crucial for accurate diagnosis and management.
• The association of PLSVC with congenital heart disease underscores the need for comprehensive cardiac evaluation.
• This case contributes to the limited understanding of the clinical significance and management of combined rare venous anomalies.