Glomus tumor in the lung parenchyma

Glomus tumors are uncommon lesions of glomus cell origin with ultrastructural and immunohistochemical features of smooth muscle. In the majority of the cases reported in the literature glomus tumors are benign, but there are some rare cases in which they demonstrate aggressive and malignant clinical and histological features. Glomangiosarcomas of the lung are extremely rare malignant tumors, because of the fact that glomus bodies are rare or absent. Due to their rarity they are misdiagnosed. Surgical resection is considered to be the most effective treatment for this condition. We report a case of a 35 year old female with a pulmonary glomangiosarcoma.