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Mature orbital teratoma with an ectopic tooth and primary anophthalmos
Bhavna Chawla1, Kanchan Chauhan, Seema Kashyap
1Oculoplastics, Orbit & Ocular Oncology Service, All India Institute of Medical Sciences, New Delhi, India. bhavna2424@hotmail.com
Purpose:
To describe the clinicopathologic features and management of an unusual case of orbital teratoma.
Methods:
A 7-year-old girl presented with a history of an orbital mass since birth. CT scan showed a large mass lesion involving the right orbit, with absence of the eyeball. An ectopic tooth was identified within the tumor. Lid-sparing exenteration surgery was performed.
Results:
Histopathologic examination of the excised mass showed presence of elements from all three germ layers, consistent with a diagnosis of mature orbital teratoma. Normal ocular structures were not identified on histopathology. At one year follow-up, there was no tumor recurrence.
Conclusion:
We report an extremely rare and interesting case of a mature orbital teratoma, which was associated with primary anophthalmos and an ectopic tooth.
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