Congenital cystic adenomatoid malformation presenting as lung abscess in a child

K Jagadish Kumar1, M G Anilkumar, Y L Shivamurthy

  • 1Department of Pediatrics, JSS Medical College, Mysore, India. jagdishmandya@gmail.com

Tuberkuloz Ve Toraks
|January 8, 2013
PubMed

Insights

Congenital cystic adenomatoid malformation (CCAM) can present atypically in older children. This case highlights CCAM mimicking empyema in a 3-year-old, requiring surgical intervention.

Area of Science:

  • Pediatric Pulmonology
  • Thoracic Surgery
  • Medical Imaging

Background:

  • Congenital cystic adenomatoid malformation (CCAM) involves hamartomatous cystic lung lesions with abnormal bronchiolar structures.
  • Typically presents with neonatal respiratory distress or early childhood infections, diagnosed before age two.

Observation:

  • A 3-year-old male presented with symptoms mimicking empyema, specifically a lung abscess.
  • This atypical presentation delayed the diagnosis of CCAM.

Findings:

  • The patient was diagnosed with congenital cystic adenomatoid malformation.
  • Surgical lobectomy was performed to treat the lung abscess caused by CCAM.

Implications:

  • CCAM can present with unusual clinical manifestations in older children, challenging early diagnosis.
  • Prompt surgical management, such as lobectomy, is effective for CCAM presenting as lung abscess.
  • Highlights the importance of considering rare diagnoses in pediatric respiratory conditions.

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