Non-compaction of the left ventricular myocardium with cor-triatriatum and associated anomalies

Non-compaction of ventricular myocardium (NVM) is a rare clinical entity. It has been reported more frequently in recent years because of continuous improvements in imaging techniques and resolution. Although apical region of the left ventricle is the most commonly involved site, biventricular involvement has also been reported in the published literature. This abnormality is often associated with other congenital cardiac and extracardiac anomalies. We describe such a case, incidentally detected and documented by the combination of echocardiography and multidetector CT coronary angiography. In our case, NVM was associated with Cor-triatriutum, ventricular septal defect, persistent left superior vena cava and an anomalous extracardiac vessel. Synchronous association of all these anomalies in a child has never been reported in the literature.