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08:19
A Pipeline to Characterize Structural Heart Defects in the Fetal Mouse
Published on: December 16, 2022
Complex Ebstein's malformation: defining preoperative cardiac anatomy and function
Ruxandra Irina Negoi1, Alexandru Teodor Ispas, Ioana Ghiorghiu
1Universityof Medicine and Pharmacy Carol Davila, Bucharest, Romania. negoiruxandra@gmail.com
Journal of Cardiac Surgery
|January 22, 2013
Summary
Advancements in 3D echocardiography and cardiac MRI improve understanding of Ebstein's malformation. This leads to more valve-sparing surgeries and reduced mortality for this rare congenital heart defect.
Area of Science:
- Cardiology
- Medical Imaging
- Congenital Heart Disease
Background:
- Ebstein's malformation is a rare congenital heart defect affecting the tricuspid valve and right ventricle.
- It presents with highly variable morphology and clinical symptoms, accounting for <1% of all congenital heart diseases.
Purpose of the Study:
- To review the progress of imaging techniques for Ebstein's malformation.
- To understand the impact of imaging on preoperative planning and surgical outcomes.
Main Methods:
- Systematic review of English language literature.
- Focused on echocardiography and cardiac magnetic resonance imaging.
- Utilized MEDLINE database via PubMed Entre.
Main Results:
- 3D echocardiography and cardiac MRI enhance in vivo anatomical understanding of the malformed tricuspid valve and right ventricle.
- Improved understanding drives a trend towards tricuspid valve-sparing procedures.
- This shift correlates with decreased early and late postoperative mortality.
Conclusions:
- Imaging techniques for Ebstein's malformation have significantly evolved.
- Standardization of assessment protocols for 3D echocardiography, speckle tracking, and cardiac MRI is necessary.
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