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First case of intracardiac foregut cyst occurring in the left-ventricular outflow tract

Jennifer H Huang1, Erin R Rudzinski, Mary S Minette

  • 1Department of Pediatric Cardiology, Doernbecher Children's Hospital, 3604 SE Morrison Street, Portland, OR, 97239, USA, jenniferhhuang@gmail.com.

Pediatric Cardiology
|January 24, 2013
PubMed

Insights

A rare intracardiac foregut cyst caused critical aortic stenosis and left-ventricular outflow obstruction (LVOT) in an infant. This case highlights the potential for foregut cysts to cause severe cardiac issues, necessitating surgical intervention.

Area of Science:

  • Pediatric Cardiology
  • Congenital Heart Disease
  • Surgical Pathology

Background:

  • Critical aortic stenosis in neonates often requires surgical intervention.
  • Left-ventricular outflow obstruction (LVOT) is a significant concern in pediatric cardiac patients.
  • Intracardiac masses are uncommon causes of congenital heart defects.

Observation:

  • An 11-day-old infant presented with subaortic mass and critical aortic stenosis.
  • Recurrent severe LVOT and heart failure occurred at 3 months of age.
  • Redo surgery revealed an intracardiac foregut cyst as the obstructing mass.

Findings:

  • The resected mass was identified as an intracardiac foregut cyst.
  • This cyst was the cause of both initial critical aortic stenosis and subsequent recurrent LVOT.
  • This represents the first reported case of an intracardiac foregut cyst causing LVOT.

Implications:

  • Foregut cysts should be considered in the differential diagnosis of neonatal cardiac masses and outflow obstruction.
  • Early diagnosis and surgical management are crucial for improving outcomes in affected infants.
  • This case expands the understanding of rare causes of congenital heart disease and LVOT.

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