Aortic valve replacement for aortic stenosis caused by alkaptonuria.

Junko Hiroyoshi1, Aya Saito, Nirmal Panthee

  • 1Department of Cardiothoracic Surgery, the University of Tokyo, Faculty of Medicine, Tokyo, Japan.

Summary

This case study details a 70-year-old man with aortic stenosis and ochronosis who received a biologic aortic valve replacement. Intraoperative findings revealed a calcified, pigmented aortic valve and aortic intima consistent with ochronosis.

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