Alive with almost no Brain: Severe Post-Hemorrhagic Internal Hydrocephalus

Area of Science:

• Neurology
• Pediatric Neurology
• Neuroscience

Background:

• Severe post-hemorrhagic internal hydrocephalus is a rare condition.
• Characterized by significant cerebral parenchyma atrophy.
• Often associated with developmental delays and neurological deficits.

Observation:

• A 19-year-old female with a history of premature birth and intraventricular bleeding presented with seizures.
• Imaging revealed massive internal hydrocephalus with widespread cerebral atrophy.
• The patient exhibited severe mental retardation, motor deficits, and tetraspasticity.

Findings:

• The patient's condition, despite severe brain atrophy, was managed without surgical intervention like a shunt.
• The hydrocephalus and atrophy manifested as psychomotor retardation, epilepsy, and tetraspasticity.
• The patient was able to sit, eat, and produce sounds, indicating some level of functional capacity.

Implications:

• This case demonstrates that severe post-hemorrhagic internal hydrocephalus with profound cerebral atrophy is compatible with life.
• Highlights the importance of long-term management and supportive care in such rare neurological conditions.
• Suggests potential for survival and a degree of functional capacity even with extensive neurological damage.