Isolated interrupted aortic arch in an 18-year-old man

Area of Science:

• Cardiology
• Congenital Heart Disease
• Adult Congenital Heart Surgery

Background:

• Isolated interrupted aortic arch is a rare congenital malformation, seldom diagnosed in adulthood.
• Adult presentations typically involve Type A interruption without ventricular septal defects.
• Surgical repair in adults is complicated by extensive collateral circulation.

Observation:

• A successful single-staged, extra-anatomic ventral aortic repair was performed on an 18-year-old male with Type A interrupted aortic arch.
• This approach addressed the challenges posed by collateral circulation in an adult patient.
• The case highlights the possibility of surgical intervention in adult patients with this condition.

Findings:

• The extra-anatomic ventral aortic repair proved effective for Type A interrupted aortic arch in an adult.
• This surgical strategy offers a viable alternative for complex congenital heart anomalies.
• The study contributes to understanding the pathogenesis of the adult form of interrupted aortic arch.

Implications:

• This successful repair suggests that surgical intervention for adult interrupted aortic arch is feasible.
• The findings may encourage the development of new surgical techniques for rare adult congenital heart diseases.
• Further research into the long-term outcomes of this repair is warranted.