Midline segmental odontomaxillary dysplasia

Area of Science:

• Dentistry
• Oral and Maxillofacial Surgery
• Developmental Biology

Background:

• Segmental odontomaxillary dysplasia (SOD) is a rare developmental disorder of the maxilla.
• It presents with variable clinical and radiological features, often mimicking other fibro-osseous lesions.
• Typically diagnosed in early childhood, SOD involves unilateral alveolar process expansion, gingival enlargement, premolar absence, delayed eruption, and primary molar malformations.

Observation:

• A rare case of SOD is described in a 19-year-old female.
• The patient presented with pre-maxillary enlargement and an abnormal eruption pattern of anterior maxillary permanent teeth.
• This marks the first reported instance of SOD occurring along the midline.

Findings:

• Radiographic imaging revealed abnormal bony trabeculation in the affected maxilla.
• Histopathologic examination confirmed the characteristic features of SOD.
• The case aligns with previous reports but extends the known presentation of SOD to the midline.

Implications:

• This case expands the spectrum of clinical presentations for Segmental Odontomaxillary Dysplasia.
• Awareness of midline SOD is crucial for accurate diagnosis and management of facial asymmetry.
• Further research into the etiology and management of SOD is warranted.