A case of Stengel-Wolbach sclerosis: a half century after the last report

Stengel-Wolbach sclerosis is a rare form of granulomatosis of the lymphoid tissue, with largely predominant involvement of the spleen. Firstly described by Wolbach in 1910, it has disappeared from the literature from the beginning of the last century. Herein, we describe the case of a 29-year-old female with splenomegaly due to multiple nodular lesions. On the basis of morphological and molecular biology findings, a diagnosis of Stengel-Wolbach sclerosis of unknown aetiology was made. The presentation of this case may reopen the discussion on this enigmatic entity.