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Published on: December 9, 2016

Primary pediatric endobronchial Ewing sarcoma family of tumors

Akira Hayakawa1, Satoshi Hirase, Natsuki Matsunoshita

  • 1Department of Pediatrics, Kobe University Graduate School of Medicine, Kobe, Japan.

The American Journal of Case Reports
|April 10, 2013
PubMed

Insights

We report a rare case of primary endobronchial Ewing sarcoma family of tumors in a child. This pediatric bronchial tumor highlights the importance of considering Ewing sarcoma in differential diagnoses.

Area of Science:

  • Pediatric Oncology
  • Thoracic Surgery
  • Pathology

Background:

  • Ewing sarcoma family of tumors (ESFT) is the second most common pediatric bone tumor.
  • Extraosseous ESFT, arising in soft tissues, is rare.
  • Primary endobronchial ESFT is exceptionally rare.

Purpose of the Study:

  • To present a unique pediatric case of primary endobronchial ESFT.
  • To discuss the diagnostic considerations for bronchial tumors in children.
  • To highlight the rarity and clinical presentation of this condition.

Main Methods:

  • A 12-year-old boy presented with dyspnea and right pulmonary atelectasis.
  • Imaging revealed a tumor in the right main bronchus.
  • Histopathological examination confirmed ESFT; the bronchus was deemed the primary site.

Main Results:

  • The patient underwent tumor resection, chemotherapy, and radiotherapy.
  • After 1 year and 6 months post-treatment, the patient remains disease-free.
  • No other lesions were detected, supporting a primary endobronchial origin.

Conclusions:

  • Primary endobronchial ESFT is an extremely rare entity.
  • ESFT should be included in the differential diagnosis of pediatric bronchial tumors.
  • This case underscores the importance of thorough evaluation for rare malignancies.
Abstract

Keywords:
Ewing sarcoma family of tumorsatelectasispediatric endobronchial tumor

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