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Intrauterine volvulus with malrotation: prenatal diagnosis
C Varetti1, D Meucci, F Severi
1Department of Pediatrics, Obstetrics and Reproductive Medicine , University of Siena, Siena, Italy. messinam@unisi.it
Minerva Pediatrica
|April 25, 2013
Summary
Midgut volvulus with malrotation is a rare condition diagnosed prenatally via ultrasound. Early diagnosis and management are crucial for favorable outcomes in newborns.
Area of Science:
- Pediatric Surgery
- Fetal Medicine
- Neonatology
Background:
- Midgut volvulus involves intestinal rotation around the superior mesenteric artery, causing obstruction and ischemia.
- This rare condition affects approximately 1 in 6000 live births.
Observation:
- A case of midgut volvulus with malrotation was diagnosed prenatally at 33 weeks gestation.
- Prenatal echotomography is vital for differential diagnosis of fetal abdominal abnormalities.
Findings:
- Prenatal diagnosis of midgut volvulus enables timely intervention.
- Prognosis is influenced by remaining intestinal length, obstruction site, meconium peritonitis, and congenital anomalies.
Implications:
- Early prenatal detection of midgut volvulus improves surgical planning and neonatal care.
- Optimizing birth weight and minimizing prematurity are key factors for better patient outcomes.

