Mitral valve endocarditis in a patient with Ehlers-Danlos syndrome

We report a patient with Ehlers-Danlos syndrome and mitral valve endocarditis. The case was complicated due to the initial septic status of the patient and the fragility of the mitral valve both of which required further early operative intervention. The patient also had pre-existing pulmonary septic emboli, the significance of which was missed prior to the admission to our Unit. Two peripheral arterial aneurysms were identified and corrected surgically on same admission. Possible complications of the syndrome and surgical implications are discussed along with review of the literature.