Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Related Experiment Videos

Temperament in Williams syndrome.

S A Tomc1, N K Williamson, R M Pauli

  • 1Department of Medical Genetics, University of Wisconsin, Madison.

American Journal of Medical Genetics
|July 1, 1990
PubMed
Summary

Children with Williams syndrome exhibit distinct temperaments, including high activity and approach behaviors. Understanding these behavioral styles helps parents manage challenges and foster positive parent-child interactions.

Related Concept Videos

You might also read

Related Articles

Articles linked to this work by shared authors, journal, and citation graph.

Sort by
Same author

A phenotype intermediate between Desbuquois dysplasia and diastrophic dysplasia secondary to mutations in DTDST.

American journal of medical genetics. Part A·2008
Same author

Microdissection-based high-resolution genomic array analysis of two patients with cytogenetically identical interstitial deletions of chromosome 1q but distinct clinical phenotypes.

American journal of medical genetics. Part A·2006
Same author

An analysis of PAX1 in the development of vertebral malformations.

Clinical genetics·2005
Same author

Prenatal diagnosis of isolated femoral bent bone skeletal dysplasia: problems in differential diagnosis and genetic counseling.

American journal of medical genetics. Part A·2003
Same author

Klippel-Feil anomaly with Sprengel anomaly, omovertebral bone, thumb abnormalities, and flexion-crease changes: novel association or syndrome?

American journal of medical genetics·2001
Same author

Hajdu--Cheney syndrome: evolution of phenotype and clinical problems.

American journal of medical genetics·2001

Area of Science:

  • Developmental Psychology
  • Behavioral Genetics

Background:

  • Anecdotal evidence suggests unique temperaments in children with Williams syndrome.
  • Williams syndrome is a genetic disorder associated with characteristic behavioral and cognitive profiles.

Purpose of the Study:

  • To objectively assess the temperament of children with Williams syndrome.
  • To compare the temperament of children with Williams syndrome to the general population.

Main Methods:

  • Utilized standard temperament scales based on parental responses.
  • Analyzed behavioral style across multiple dimensions including activity, mood, and adaptability.

Main Results:

  • Children with Williams syndrome displayed higher activity, lower rhythmicity, greater approach, lower adaptability, greater intensity, more negative mood, less persistence, greater distractibility, and lower arousal threshold compared to average children.
  • Despite being classified as 'difficult,' these children showed an approaching rather than withdrawing tendency.
  • Older children with Williams syndrome were more likely to be perceived as 'difficult.'

Conclusions:

  • Williams syndrome is associated with a specific, often challenging, temperament profile.
  • Parents require education on these temperament characteristics and effective interaction strategies.
  • Intervention should focus on modifying parent-child interactions to accommodate the child's behavioral style.

Related Experiment Videos