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Updated: May 11, 2026

Imaging Features of Systemic Sclerosis-Associated Interstitial Lung Disease
Published on: June 16, 2020
Imaging of scleroderma
1Department of Radiology and Radiological Science, Medical University of South Carolina, Charleston, SC 29425, USA. chapinrw@musc.edu
Systemic sclerosis, a rare autoimmune disease, impacts multiple organs. This review details common and rare imaging findings across various systems to aid diagnosis and treatment planning.
Area of Science:
- Radiology
- Autoimmune Diseases
- Systemic Sclerosis Imaging
Background:
- Systemic sclerosis is a rare autoimmune disorder affecting multiple organ systems.
- Accurate diagnosis and treatment guidance rely on understanding its diverse imaging features.
- This review focuses on the radiological manifestations of systemic sclerosis.
Purpose of the Study:
- To comprehensively review the common and rare imaging features of systemic sclerosis.
- To cover imaging findings in skin, musculoskeletal, pulmonary, cardiac, gastrointestinal, renal, and oral systems.
- To discuss conventional and advanced imaging modalities for systemic sclerosis.
Main Methods:
- Review of common and rare imaging features in systemic sclerosis.
- Discussion of conventional radiography, CT chest, echocardiography, enterography, scintigraphy, and dental imaging.
- Exploration of emerging roles for ultrasonography and MRI in musculoskeletal and cardiac assessment.
Main Results:
- Detailed review of imaging findings across multiple organ systems affected by systemic sclerosis.
- Inclusion of both conventional and advanced imaging techniques.
- Emphasis on the diagnostic and therapeutic implications of identified imaging features.
Conclusions:
- Understanding systemic sclerosis imaging features is crucial for diagnosis and management.
- A wide range of imaging modalities are employed to evaluate affected organ systems.
- Emerging technologies like ultrasonography and MRI offer new insights into musculoskeletal and cardiac involvement.
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