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[Junctional syndrome responsible for prostatic urethral dilatation: a new pathological entity?]
J L'Hermite1, A Six, M Schmitt
1Service d'urologie, CHR Nancy-Brabois, Vandoeuvre-les-Nancy.
Summary
Monstrous prostatic urethral ectasia in boys can cause severe urinary retention. Surgical and minimally invasive treatments targeting the urethra successfully resolved symptoms and restored normal function.
Area of Science:
- Pediatric Urology
- Urethral Pathologies
- Functional Urology
Background:
- Monstrous ectasia of the prostatic urethra is a rare condition.
- Typically presents with severe urinary retention and dysuria in young boys.
- Etiology often relates to functional rather than organic obstruction.
Observation:
- Two cases of 12-year-old boys with no prior history presented with significant urinary retention (500ml and 1250ml).
- Initial investigations suggested potential vesico-sphincter dyssynergia or sphincter hypertension.
- Symptoms were attributed to intrinsic urethral functional disorders.
Findings:
- Case 1: Complex surgery involving urethral ectasia reduction and reimplantation achieved immediate complete bladder emptying and normalized flowmetry within six months.
- Case 2: Sub-montanal urethrotomy resulted in complete bladder emptying within ten months.
- Both patients maintained functional recovery at nine and two years post-treatment.
Implications:
- Successful treatment outcomes suggest intrinsic urethral pathology as a primary cause.
- Urethral-focused treatments can effectively manage severe prostatic urethral ectasia.
- Preservation of the striated sphincter is crucial for successful functional recovery.