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Behçet's disease presenting with Budd-Chiari syndrome and intracardial thrombus: a case report

Minji Jennifer Kim1, Yong Suk Jo, Jee Hyun Kim

  • 1School of Medicine, University of Manchester, Manchester, UK.

International Medical Case Reports Journal
|June 12, 2013
PubMed

Insights

Budd-Chiari syndrome is a rare complication of Behçet

Area of Science:

  • Vascular Medicine
  • Rheumatology
  • Cardiology

Background:

  • Behçet's disease is a chronic inflammatory disorder with potential vascular complications.
  • Budd-Chiari syndrome, a rare hepatic venous outflow obstruction, can manifest as a late complication of Behçet's disease.
  • Intracardial thrombus formation can further elevate mortality in these patients.

Observation:

  • This case report details an unusual presentation of Behçet's disease.
  • The patient, a young Korean man, developed Budd-Chiari syndrome.
  • The syndrome was complicated by the formation of an intracardial thrombus.

Findings:

  • Early detection and management are critical for improving outcomes in Behçet's disease with Budd-Chiari syndrome.
  • Minimally invasive imaging modalities are preferred to avoid aggravating thrombosis.
  • Cardiac investigation is essential to identify cardiac involvement and thrombus etiology.

Implications:

  • Controlling Behçet's disease activity is paramount for effective treatment.
  • This case highlights the importance of a comprehensive work-up, including cardiac assessment, in patients with Behçet's disease and Budd-Chiari syndrome.
  • Understanding this rare association can guide clinical management and improve patient prognosis.

Keywords:
Behçet’s diseaseBudd-Chiari syndromeintracardial thrombus

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