Chylous jejunal cyst causing volvulus in a child: case report and literature review

Liliana Guzmán1, Eittel Oppenheimer, Humberto Lugo-Vicente

  • 1Department of Pediatrics and Residency Program, San Juan City Hospital, San Juan, Puerto Rico.

Insights

Chylous jejunal cysts are rare but can cause serious complications. Prompt diagnosis and surgical intervention, like resection and detorsion, are crucial for treating this condition in pediatric patients.

Area of Science:

  • Gastroenterology
  • Pediatric Surgery
  • Surgical Pathology

Background:

  • Chylous jejunal cysts are exceptionally rare congenital anomalies.
  • Delayed diagnosis can lead to severe complications, including bowel obstruction, small bowel loss, and mortality.

Observation:

  • A 4-year-old male presented with severe abdominal pain, constipation, and distention.
  • Radiological imaging revealed significant abdominal fluid and bowel obstruction.

Findings:

  • Intraoperative findings identified a large chylous jejunal cyst causing segmental volvulus.
  • Surgical management involved resection of the affected jejunal segment and cyst, along with detorsion.

Implications:

  • This case highlights the importance of early recognition and surgical management of chylous jejunal cysts.
  • Prompt intervention can prevent life-threatening complications in pediatric patients with this rare condition.

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