Unilateral pulmonary artery agenesis with vertebral anomaly
Rajniti Prasad1, G N Srivastava, O P Mishra
1Department of Pediatrics, Institute of Medical Sciences, Varanasi, Uttar Pradesh, India.
BMJ Case Reports
|June 21, 2013
Abstract:
We report a two-and-half-year-old boy who presented with recurrent respiratory tract infections. He had cortriatum of right atrium, spina bifida occulta, hemivertebra and dysplastic right thumb. On CT of chest, he had also unilateral pulmonary artery agenesis. The case is being reported because of common manifestations of rare disease and its associated cardiac and skeletal abnormalities.
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