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Ventricular arrhythmias due to left ventricular noncompaction cardiomyopathy: a diagnosis in hindsight

Jackson J Liang1, Kyle M McKenzie1, Yong-Mei Cha2

  • 1Department of Medicine, Mayo Clinic, Rochester, MN, USA.

Heart, Lung & Circulation
|June 25, 2013
PubMed

Insights

Left ventricular noncompaction cardiomyopathy is a rare congenital heart condition. This case highlights its diagnosis in a young man with a history of ventricular tachycardia and an implantable cardioverter-defibrillator.

Area of Science:

  • Cardiology
  • Genetics
  • Pathology

Background:

  • Left ventricular noncompaction cardiomyopathy (LVNC) is a rare congenital cardiomyopathy.
  • It is characterized by excessive trabeculation and deep recesses in the left ventricle.
  • LVNC is associated with an increased risk of heart failure, arrhythmias, and sudden cardiac death.

Observation:

  • A 24-year-old man with a history of sustained ventricular tachycardia requiring an implantable cardioverter-defibrillator (ICD) presented with a device infection.
  • During hospitalization for the infection, diagnostic workup revealed findings consistent with LVNC.

Findings:

  • The patient was diagnosed with left ventricular noncompaction cardiomyopathy.
  • This diagnosis was made subsequent to his initial presentation and treatment for ventricular tachycardia and ICD placement.

Implications:

  • This case underscores the importance of considering LVNC in young individuals with unexplained ventricular arrhythmias and cardiac devices.
  • Early diagnosis and appropriate management of LVNC are crucial for preventing adverse cardiovascular events.
  • Further research into the genetic basis and long-term outcomes of LVNC is warranted.

Keywords:
ArrhythmiaCardiac MRIDilated cardiomyopathyImplantable cardioverter-defibrillatorLeft ventricular noncompaction cardiomyopathyVentricular tachycardia

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