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[Diffuse esophageal leiomyomatosis. Apropos of 3 cases]
Y Heloury1, J L Borgne, J M Babut
1Service de Chirurgie Infantile, Nantes.
Chirurgie Pediatrique
|January 1, 1990
Abstract:
Three cases of diffuse esophageal leiomyomatosis are discussed. Two of these are familial one, the mother being affected. These familial cases can occur in association with Alport's syndrome. The occurrence of a case of esophageal leiomyomatosis imply a familial survey and the search of a renal or ocular disease. The surgical treatment of this affection in sub total oesophagectomy with esophageal substitution (with the colon especially). The long term prognosis is unknown, with the risk of renal failure if Alport's syndrome is associated or of other leiomyomatous localisation.