Nevus of hoffmann-zurhelle: a case around the right parotid duct

Nevus lipomatosus cutaneous superficialis (NLCS) is an extremely rare hamartomatous disorder comprising of ectopic mature adipose tissue. The lesions take the form of large, slow-growing, sessile or pedunculated tumors. We report the case of an 11-year-old boy with NLCS, dating back many months, that was growing as a cuff around the parotid duct. The lesion was successfully removed by diode laser excision (980 nm) and a diagnosis of NLCS was rendered. At one-year follow-up the tumor has not recurred. To our knowledge this is the first report of NLCS in the oral cavity; the characteristic clinical and morphological features aided in the diagnosis of this hamartoma. The peculiarity of this case is its location; the extreme rarity of NLCS, in general, probably makes this case unique.