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Increased aggregation of polyleucine compared with that of polyglutamine in dentatorubral-pallidoluysian atrophy

Yasuyo Suzuki1, Chenghua Jin, Ikuru Yazawa

  • 1Laboratory of Research Resources, Research Institute for Longevity Sciences, National Center for Geriatrics and Gerontology, Aichi 474-8511, Japan.

Neuroscience Letters
|August 13, 2013
PubMed

Keywords:
ATN1Atrophin-1CNSDRPLADentatorubral-pallidoluysian atrophyHDHuntington's diseaseN,N,N′,N′-tetrakis (2-pyridylmethyl) ethylenediamineNeurodegenerationPolyglutaminePolyleucineSCATPENZ-VAD-FMKatrophin-1benzyloxycarbonyl-Val-Ala-Asp(OMe)-fluoromethyl ketone.central nervous systemdentatorubral-pallidoluysian atrophypolyLpolyQpolyglutaminepolyleucinespinocerebellar ataxia

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