Arthrocutaneous haemangiomatosis with destructive arthritis

A case of synovial haemangiomatosis of the knee joint with associated severe destructive arthritis is reported. The patient also had widespread cutaneous port wine stains and a bilateral Naevus of Ota. The interesting association between cutaneous and synovial haemangiomatosis is discussed. A pathogenic association of synovial haemangiomatosis and destructive arthritis is offered. Patients presenting with port wine stains and joint symptoms should be considered for the investigation of synovial haemangiomatosis.