Growing bilateral occipital calcifications and epilepsy

Recently presented data have allowed us to detect an increasing number of cases which present bilateral occipital calcifications and epilepsy or migraine. They have been indicated for the most part to have atypical forms of Sturge-Weber disease without facial nevus flammeus. Two pediatric patients are dealt with here, who, while presenting some differences from the electroclinical point of view, are characterized by typical cortico-subcortical bilateral occipital growing calcifications. Generally, other authors consider the first phase of this syndrome to comprise benign development; only in a second phase does worsening of the fits follow, as well as a bad prognosis. On the contrary, in our case up to now, the patients have been well; the seizures are under control with AEDs and EEG has not worsened, in spite of growing occipital calcifications.