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Updated: May 7, 2026

In Vivo Electrophysiological Measurement of Compound Muscle Action Potential from the Forelimbs in Mouse Models of Motor Neuron Degeneration
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Published on: June 15, 2018

Inherited neuropathies: an update.

Anna Sagnelli1, Giuseppe Piscosquito, Davide Pareyson

  • 1Clinic of Central and Peripheral Degenerative Neuropathies Unit, Department of Clinical Neurosciences, IRCCS Foundation, "C. Besta" Neurological Institute, via Celoria 11, 20133, Milan, Italy.

Journal of Neurology
|September 25, 2013
PubMed
Summary
This summary is machine-generated.

This review summarizes recent hereditary neuropathy research from the Journal of Neurology. It covers key advancements in understanding and treating these genetic nerve disorders.

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Related Experiment Videos

Last Updated: May 7, 2026

In Vivo Electrophysiological Measurement of Compound Muscle Action Potential from the Forelimbs in Mouse Models of Motor Neuron Degeneration
06:35

In Vivo Electrophysiological Measurement of Compound Muscle Action Potential from the Forelimbs in Mouse Models of Motor Neuron Degeneration

Published on: June 15, 2018

In Vivo Electrophysiological Measurement of the Rat Ulnar Nerve with Axonal Excitability Testing
04:56

In Vivo Electrophysiological Measurement of the Rat Ulnar Nerve with Axonal Excitability Testing

Published on: February 6, 2018

Area of Science:

  • Neurology
  • Genetics
  • Hereditary Neuropathies

Background:

  • Hereditary neuropathies encompass a group of genetic disorders affecting peripheral nerves.
  • Understanding the genetic basis and clinical manifestations is crucial for diagnosis and treatment.

Purpose of the Study:

  • To provide a concise overview of the latest research findings in hereditary neuropathy.
  • To highlight significant progress published in the Journal of Neurology over the past 18 months.

Main Methods:

  • Systematic review of articles published in the Journal of Neurology.
  • Focus on research concerning hereditary neuropathies within the specified timeframe.

Main Results:

  • Key advancements in genetic discoveries related to hereditary neuropathies.
  • New insights into disease mechanisms and potential therapeutic targets.
  • Updates on diagnostic approaches and clinical management strategies.

Conclusions:

  • The field of hereditary neuropathy research is rapidly evolving.
  • Continued investigation is vital for improving patient outcomes and developing effective therapies.