Infantile extrapancreatic pancreatoblastoma: a report on a rare infantile abdominal mass

Hossein Esfahani1, Elham Olad, Arash Dehghan

  • 1Departments of *Pediatric Hematology/Oncology †Pediatrics ‡Pathology §Pediatric Gastroenterology, Hamadan University of Medical Science, Hamadan, Islamic Republic of Iran.

Insights

This report details a rare case of pancreatoblastoma in a 3-month-old infant. The tumor, found outside the pancreas, was successfully resected, highlighting early detection and surgical intervention for pediatric abdominal masses.

Area of Science:

  • Pediatric Oncology
  • Surgical Pathology

Background:

  • Pancreatoblastoma is an exceptionally rare pediatric tumor, with even rarer occurrences in infants under three months.
  • Ectopic pancreatic tissue can serve as a site for tumor origin, complicating diagnosis and surgical planning.

Observation:

  • A 3-month-old male presented with a large abdominal mass.
  • CT imaging identified a lobulated mass anterior to the kidneys, featuring calcification and contrast enhancement.
  • The mass was surgically resected from the transverse mesocolon, separate from the pancreas.

Findings:

  • Pathological examination confirmed the diagnosis of pancreatoblastoma.
  • The tumor's extra-pancreatic origin was a notable characteristic.

Implications:

  • This case underscores the importance of considering rare diagnoses like pancreatoblastoma in infants with abdominal masses.
  • Complete surgical resection is a viable primary treatment, even for extra-pancreatic pancreatoblastomas.
  • The successful outcome emphasizes the need for vigilant postsurgical follow-up in pediatric oncology cases.